Feasibility of a single-port thoracoscopy-assisted five-step laparoscopic procedure via transabdominal diaphragmatic approach for No.111 lymphadenectomy in patients with Siewert type II esophageal gastric junction adenocarcinoma / 中华胃肠外科杂志

Objective: We aimed to explore the feasibility of a single-port thoracoscopy- assisted five-step laparoscopic procedure via transabdominal diaphragmatic(TD) approach(abbreviated as five-step maneuver) for No.111 lymphadenectomy in patients with Siewert type II esophageal gastric junction adenocarcinoma (AEG). Methods: This was a descriptive case series study. The inclusion criteria were as follows: (1) age 18-80 years; (2) diagnosis of Siewert type II AEG; (3) clinical tumor stage cT2-4aNanyM0; (4) meeting indications of the transthoracic single-port assisted laparoscopic five-step procedure incorporating lower mediastinal lymph node dissection via a TD approach; (5) Eastern Cooperative Oncology Group performance status (ECOG PS) 0-1; and (6) American Society of Anesthesiologists classification I, II, or III. The exclusion criteria included previous esophageal or gastric surgery, other cancers within the previous 5 years, pregnancy or lactation, and serious medical conditions. We retrospectively collected and analyzed the clinical data of 17 patients (age [mean ± SD], [63.6±11.9] years; and 12 men) who met the inclusion criteria in the Guangdong Provincial Hospital of Chinese Medicine from January 2022 to September 2022. No.111 lymphadenectomy was performed using five-step maneuver as follows: superior to the diaphragm, starting caudad to the pericardium, along the direction of the cardio-phrenic angle and ending at the upper part of the cardio-phrenic angle, right to the right pleura and left to the fibrous pericardium , completely exposing the cardio-phrenic angle. The primary outcome includes the numbers of harvested and of positive No.111 lymph nodes. Results: Seventeen patients (3 proximal gastrectomy and 14 total gastrectomy) had undergone the five-step maneuver including lower mediastinal lymphadenectomy without conversion to laparotomy or thoracotomy and all had achieved R0 resection with no perioperative deaths. The total operative time was (268.2±32.9) minutes, and the lower mediastinal lymph node dissection time was (34.0±6.0) minutes. The median estimated blood loss was 50 (20-350) ml. A median of 7 (2-17) mediastinal lymph nodes and 2(0-6) No. 111 lymph nodes were harvested. No. 111 lymph node metastasis was identified in 1 patient. The time to first flatus occurred 3 (2-4) days postoperatively and thoracic drainage was used for 7 (4-15) days. The median postoperative hospital stay was 9 (6-16) days. One patient had a chylous fistula that resolved with conservative treatment. No serious complications occurred in any patient. Conclusion: The single-port thoracoscopy-assisted five-step laparoscopic procedure via a TD approach can facilitate No. 111 lymphadenectomy with few complications.

Vascular and ventilatory mechanical responses in three different stages of pulmonary development in the rabbit model of congenital diaphragmatic hernia

Abstract Purpose: To evaluate the vascular ventilatory response in different stages of lung development and to compare them to the neonates with congenital diaphragmatic hernia (CDH) in a rabbit model. Methods: New Zealand rabbits were divided into 8 groups (n=5): E25, E27, E30, and CDH. All groups were ventilated on a FlexiVent (Scireq, Montreal, QC, Canada), compounding the other 4 groups. The CDH surgery was performed at E25 and the harvest at E30. Dynamic compliance (CRS), dynamic elastance (ERS) and dynamic resistance (RRS) were measured every 4 min/24 min. Median wall thickness (MWT) and airspace were measured. ANOVA Bonferroni tests were used to perform statistical analysis. Significance was considered when p<0.05. Results: CRS was higher in E30 compared to all other groups (p<0.05). CRS and RRS of CDH and E27 were similar and were higher in E25 (p<0.05). MWT was decreased according to the gestational age, was increased in E27V and E30V (p<0.05) and decreased in CDHV (p<0.05), airspace was decreased in E25 and increased in all ventilated groups (p<0.05). Conclusions: The ventilation response of congenital diaphragmatic hernia is like the pseudoglandular stage of the lung development. These findings add information about the physiology of pulmonary ventilation in CDH.

Análise retrospectiva de 103 casos de lesão diafragmática operados em um centro de trauma / Retrospective analysis of 103 diaphragmatic injuries in patients operated in a trauma center

RESUMO Objetivo: analisar os fatores associados ao óbito em pacientes com lesão diafragmática atendidos em hospital de referência para o trauma. Métodos: estudo retrospectivo de pacientes com lesão do diafragma atendidos no Hospital Risoleta Tolentino Neves da Universidade Federal de Minas Gerais entre janeiro de 2010 e dezembro de 2014. Foi utilizado o Banco de Registros de Trauma Collector® (MD, USA). Utilizaram-se dados demográficos, localização da lesão diafragmática, lesões associadas de outros órgãos, número de lesões associadas, tipo de abordagem terapêutica, complicações e o escore de gravidade Injury Severity Score (ISS). A variável de interesse foi a ocorrência de óbito. Resultados: foram identificados 103 pacientes e a incidência de óbito foi de 16,5%. Lesões penetrantes ocorreram em 98% dos pacientes. Em análise univariada a mortalidade foi maior em pacientes cujo tratamento foi não operatório, sem rafia (p=0,023), e menor em pacientes submetidos à rafia diafragmática (p<0,001). O aumento do número de lesões associou-se ao aumento da incidência de óbitos (p=0,048). Em análise multivariada, ISS>24 (OR=4,0; p=0,029) e rafia do diafragma (OR=0,76; p<0,001) associaram-se à mortalidade. Conclusão: os achados indicam que a ruptura traumática do diafragma raramente se apresenta como lesão isolada, estando associada frequentemente à lesão de outros órgãos, especialmente fígado e vísceras ocas. Pode-se afirmar que a mortalidade foi mais elevada entre aqueles com ISS>24.

ABSTRACT Objective: to analyze the factors associated with death in patients with diaphragmatic injury treated at a trauma reference hospital. Methods: we conducted a retrospective study of patients with diaphragm injury attended at the Risoleta Tolentino Neves Hospital of the Federal University of Minas Gerais, between January 2010 and December 2014. We used The Collector® database of trauma records (MD, USA). We gathered data on demographics, location of the diaphragmatic lesion, site and number of associated lesions, type of therapeutic approach, complications and Injury Severity Score (ISS). The variable of interest was the occurrence of death. Results: we identified 103 patients and mortality was 16.5%. Penetrating lesions occurred in 98% of patients. Univariate analysis showed a mortality higher in patients whose treatment was non-operative, without closing of the defect (p=0.023), and lower in patients submitted to diaphragmatic suturing (p<0.001). The increase in the number of lesions was associated with an increase in mortality (p=0.048). In multivariate analysis, ISS>24 (OR=4.0, p=0.029) and diaphragmatic suturing (OR=0.76, p<0.001) were associated with mortality. Conclusion: The findings indicate that the traumatic rupture of the diaphragm rarely presents as an isolated lesion, being frequently associated with injuries of other organs, especially the liver and hollow viscera. Mortality was higher among those with ISS>24.

Repair of penetrating pericardial and diaphragmatic injury with cormatrix® patch in a case of suicide attempt

Abstract The authors report the case of a suicide attempt. A 59-year-old man with self-inflicted penetrating chest trauma underwent emergency cardiothoracic surgery. Pre-operative computed tomography scan showed critical proximity between the blade and the right ventricle. Intraoperative findings showed a pericardial laceration and a huge diaphragmatic lesion with heart and abdominal organs integrity. The diaphragm muscle was repaired with a CorMatrix® patch, an acceptable alternative to the traditional synthetic mesh avoiding infection and repeated herniation.

Evaluation of diaphragmatic mobility following intra-abdominal sub-diaphragmatic fixation of a double-layered mesh in rats

PURPOSE: To evaluate the tissue integration of a double-sided mesh after fixation in diaphragm and to study the diaphragmatic mobility by ultrasound. METHODS: Twenty male Wistar rats were used. The animals were assigned into two equal groups according to the day of euthanasia. The animals were anesthetized and a 1.5 x 1.5 cm of double-layer mesh was inserted between the diaphragm and the liver. For the evaluation of the diaphragm mobility a sonographic method was used. Measurements on specific breathing parameters were taking place. Pathological evaluation took place after the animal's euthanasia. RESULTS: Extra-hepatic granuloma was not differentiated overtime, (χ2=0.04, p>0.05). Neither fibrosis was significantly differentiated, (χ2=0.04, p>0.05). Intra-hepatic granuloma was significantly differentiated overtime, (χ2=10.21, p<0.05). Concerning Te parameter, means were significantly differentiated over time, F (3, 30) = 5.12, (p<0.01). Ttot parameter, it was differentiated over time, F (3, 8)=4.79, (p<0.05). IR parameter was also longitudinally differentiated, F (3, 30)=3.73, (p<0.05). CONCLUSION: The measurements suggest a transient malfunction of diaphragmatic mobility despite the fact that inflammatory reaction, fibrosis and extra-hepatic granuloma were not significantly differentiated with the passage of time.

Technique for implanting intramuscular electrodes in the diaphragm by videolaparoscopy in pigs

PURPOSE: To describe a novel approach for implanting intramuscular electrodes in the diaphragm through videolaparoscopy. METHODS: We used twelve pigs for this videolaparoscopic technique, which permits at the same time to explore the diaphragm, to locate its motor points and to fix the electrodes in the diaphragm bilaterally. In this technique we used three trocars: one portal for a 10-mm 0° viewing angle laparoscope, one portal for the manipulation of structures and another for electrode implantation. RESULTS: All animals survived the procedure without pneumothorax/capnothorax or other complication. Implanted electrodes provided an appropriate interface between the muscle and the electrical current generator, and electroventilation was satisfactorily generated in all animals. CONCLUSION: This videolaparoscopic technique with three trocars enables the exploration and identification of motor points and an efficient fixation of one or two electrodes in each hemidiaphragm.

Natural history of extensive diaphragmatic injury on the right side: experimental study in rats / História natural do ferimento diafragmático extenso à direita: estudo experimental em ratos

OBJECTIVE: To evaluate the natural healing of the rat diaphragm that suffered an extensive right penetrating injury. METHODS: Animals were submitted to an extensive penetrating injury in right diaphragm. The sample consisted of 40 animals. The variables studied were initial weight, weight 21 days after surgery; healing of the diaphragm, non-healing of the diaphragm, and herniated abdominal contents into the chest. RESULTS: Ten animals were used as controls for weight and 30 animals were operated. Two animals died during the experiment, so 28 animals formed the operated group; healing of the diaphragm occurred in 15 animals (54%), 11 other animals showed diaphragmatic hernia (39%) and in two we observed only diaphragmatic injury without hernia (7%). Among the herniated organs, the liver was found in 100% of animals, followed by the omentum in 77%, small bowel in 62%, colon in 46%, stomach in 31% and spleen in 15%. The control group and the diaphragmatic healing subgroup showed increased weight since the beginning of the study and the 21 days after surgery (p <0.001). The unhealed group showed no change in weight (p = 0.228). CONCLUSION: there is a predominance of spontaneous healing in the right diaphragm; animals in which there was no healing of the diaphragm did not gain weight, and the liver was the organ present in 100% the diaphragmatic surface in all rats with healed diaphragm or not. .

OBJETIVO: avaliar a cicatrização natural do diafragma de ratos que sofreram um ferimento penetrante extenso à direita. MÉTODOS: os animais sofreram uma lesão penetrante extensa no diafragma direito. A amostra foi composta por 40 animais. As variáveis estudadas foram peso inicial e em 21 dias de operados; cicatrização do diafragma, não cicatrização do diafragma e conteúdo herniado do abdome para o tórax. RESULTADOS: dez animais constituíram o grupo controle para o peso e 30 animais foram operados. Dois animais morreram durante o experimento, sendo assim, 28 animais constituíram o grupo de operados; ocorreu a cicatrização do diafragma em 15 animais (54%), outros 11 animais apresentaram hérnia diafragmática (39%) e por fim em dois animais observamos somente lesão diafragmática sem hérnia (7%). Analisando os órgãos herniados, encontramos o fígado em 100% dos animais, seguido pelo omento em 77%; delgado em 62%; cólon em 46%; estômago em 31% e baço em 15%. Os grupos controle e de cicatrização do diafragma apresentaram acréscimo significativo de peso do momento inicial para o momento 21 dias (p<0,001). O grupo não cicatrizado não apresentou alteração de peso (p=0,228). CONCLUSÃO: há predomínio da cicatrização espontânea no diafragma à direita, os animais em que não houve a cicatrização do diafragma não aumentaram de peso, e o fígado foi o órgão 100% presente na superfície diafragmática em todos os ratos com cicatrização ou não do diafragma. .

Comparison of techniques for transdiaphragmatic thoracic drainage after diaphragmatic defect closure in dogs: a cadaveric study

Four thoracic evacuation techniques for pneumothorax elimination after diaphragmatic defect closure were compared in 40 canine cadavers. After creating a defect in the left side of the diaphragm, thoracic drainage was performed by thoracostomy tube insertion through the defect and a small (DD-SP) or large (DD-LP) puncture created in the caudal mediastinum, or through both the diaphragmatic defect and intact contralateral diaphragm with a small (DI-SP) or large (DI-LP) puncture in made in the caudal mediastinum. Differences in intrapleural pressure (IPP) between the right and left hemithoraxes after air evacuation along with differences in IPP before making a defect and after air evacuation in each hemithorax were calculated. A difference (p or = 0.0835) were observed for the DI-LP, DD-LP, or DI-SP groups. Creation of a large mediastinal puncture or thoracic evacuation through both a diaphragmatic defect and intact contralateral diaphragm can facilitate proper pneumothorax elimination bilaterally after diaphragmatic defect closure in dogs with a small puncture in the caudal mediastinum.

Toda lesão do diafragma por ferimento penetrante deve ser suturada? / Must all diaphragmatic penetrating wounds be sutured?

Os ferimentos da região tóracoabdominal podem cursar com ferimentos diafragmáticos em até 48% dos casos. Lesões associadas ao trauma diafragmático, estão presentes na maioria das vezes, o que facilita o diagnóstico da lesão diafragmática e em consequência impõe o tratamento operatório. Porém em 8 a 10% dos casos, as lesões diafragmáticas são isoladas e por apresentarem pouco ou nenhum sintoma, estas lesões podem passar despercebidas. Nestas situações, o diafragma poderia ser tratado de modo conservador, sem a sutura do mesmo? Após a realização de trabalhos experimentais com animais e de analisar a literatura, concluímos que ainda não podemos afirmar com certeza de que é possível não suturar um ferimento diafragmático.

Wounds to the abdominal-thoracic region are associated with diaphragm wounds in up to 48% of cases. Lesions secondary to diaphragm trauma are present in the majority of cases, facilitating the diagnosis of diaphragm lesion and subsequent surgical management. However, diaphragm lesions are isolated in 8 to 10% of cases and because they present few or no symptoms may be overlooked. In such situations, can the diaphragm be treated conservatively without suturing? Based on experiments in animals and a review of the literature, we concluded there is currently insufficient evidence to affirm that diaphragm injuries require no suturing.

Lesión diafragmática durante la laparoscopia urológica transperitoneal / Diaphragmatic injury during transperitoneal urological laparoscopic surgery

Introduction: Capnothorax is a rare complication of urologic laparoscopy. However with the increasing use of this technique in a variety of urological procedures, this rare complication is a potential risk. Material and Methods: We analyzed a total of 786 urological procedures performed by transperitoneal laparoscopy in our center. All procedures were performed by the same surgeon: 213 adrenalectomy, 181 simple nephrectomies, 143 lymphadenectomies, 118 radical nephrectomies, 107 partial nephrectomies and 24 nephroure-terectomy. Results: A total of 6 patients (0.7 percent) present diaphragmatic lesions. The diaphragmatic repair was performed totally intracorporeal. One patient required the placement of a pleural drainage. No patient presented complications associated with diaphragmatic injury. Conclusion: Repair of diaphragmatic injury during transperitoneal laparoscopy can be performed successfully by this route. This technique is feasible, reproducible and reliable. This is the largest series reported by a single center.

Introducción: El capnotórax es una complicación infrecuente de la laparoscopía urológica. No obstante, con el uso cada vez mayor de esta técnica en una gran variedad de procedimientos urológicos, esta infrecuente complicación se presenta como un riesgo potencial. Material y Métodos: Se analizaron un total de 786 procedimientos urológicos realizados en forma laparoscópica por vía transperitoneal en nuestro centro. Todos los procedimientos fueron realizados por el mismo cirujano: 213 adrenalectomías, 181 nefrectomías simples, 143 linfadenectomías, 118 nefrectomías radicales, 107 nefrectomías parciales y 24 nefroureterectomías. Resultados: Un total de 6 pacientes (0,7 por ciento) presentaron lesiones diafragmáticas. La reparación diafragmática fue efectuada totalmente en forma intracorpórea. Un solo paciente requirió de la colocación de un drenaje pleural. Ningún paciente presentó complicaciones asociadas a la lesión diafragmática. Conclusión: La reparación de las lesiones diafragmáticas ocurridas durante la laparoscopía transperitoneal puede ser efectuada exitosamente por esta misma vía. Esta técnica es factible, reproducible y confiable. Esta es la serie más grande reportada por un solo centro.

Traumatic rupture of diaphragm with flail chest mimicking tension hydropneumothorax.

Traumatic rupture of diaphragm though not rare, presents as complication of penetrating and blunt injuries of chest and abdomen. Preoperative diagnosis of diaphragmatic injury is difficult because of the complex shape of the thin diaphragmatic muscle, the horizontal in-plane orientation of one diaphragmatic dome, and the often associated traumatic abnormalities in the lung bases. Failure to detect this underlying injury is associated with significant morbidity and mortality because of delayed visceral herniation, strangulation or both. We report a case of left-sided post traumatic rupture of diaphragm presenting as tension hydropneumothroax following a road traffic accident. It was managed as tension hydropneumothorax during initial resuscitation by intercostal tube drainage. Lack of improvement in the clinical condition led to the suspicion of diaphragmatic rupture. The patient was managed successfully by operative repair of diaphragm and manual reduction of hernial contents

Missile diaphragmatic injuries: Kashmir experience

Importance of repairing a diaphragmatic tear due to a missile injury cannot be overemphasized.Even a small diaphragmatic rent should be repaired because of morbidity and mortality caused by subsequent herniation and strangulation. Fifty-three cases with diaphragmatic injuries caused by penetrating missiles were studied from January 1997 to January 2007. All the patients were primarily explored either for thoracic or abdominal penetrating trauma; the diaphragmatic injury was an associated incidental intraoperative finding. Thoracotomy was performed in 18 patients, Laprotomy in 33 patients and in two patients combined thorocoabdominal approach was utilised for managing associated visceral injuries. Overall mortality was 37.7%. Mortality was dependent on associated injuries of thoracic and abdominal viscera. Most patients died due to associated injuries and septicaemia. None of the patients had any sequelae of diaphragmatic repair. Immediate repair of diaphragmatic injury is of paramount importance to prevent subsequent complications of herniation and strangulation

A review on the celiac trunk compression syndrome: some anatomic clinical-surgical aspects / Una revisión del síndrome de compresión del tronco celíaco: algunos aspectos anatómicos clínicos-quirúrgicos

The objective of this study was to review some celiac trunk compression syndrome aspects such as: symptom-posture relationship; absence of symptoms; syndrome-age relationship; angiographic study on anatomy of the celiac trunk stenosis; congenital or acquired origin; invasive diagnostic tests; surgical and postoperative results.

El objetivo de este estudio fue hacer una revisión del síndrome de compresión del tronco celíaco, en cuanto a aspectos tales como: relación síntoma-postura; ausencia de síntomas; relación síndrome-edad; estudio angiográfico sobre la anatomía de la estenosis del tronco celíaco; origen congénito o adquirido; tests diagnósticos no invasivos; resultados quirúrgicos y post-quirúrgicos.

Management of diaphragmatic injury during transperitoneal laparoscopic urological procedures

INTRODUCTION: Carbon dioxide pneumothorax is a rare complication in laparoscopic urology, but with the widespread use of laparoscopy and the increasing surgical pathologies managed by this technique this infrequent complication has become a potential risk. MATERIALS AND METHODS: A total of 786 laparoscopic transperitoneal urologic operations were reviewed at our institution. All procedures were performed by the same surgeon and included 213 adrenalectomies, 181 simple nephrectomies, 143 lymphadenectomies, 118 radical nephrectomies, 107 partial nephrectomies and 24 nephroureterectomies. Mean patient age was 53.2 years (range 24 to 70). Mean BMI was 28.15 Kg/m2 (range 20 to 48.9). RESULTS: A total of 6 cases (0.7 percent) of diaphragmatic injury were found. All reported patients had additional factors that may have contributed to diaphragmatic injury. Diaphragmatic repair was always carried out by intracorporeal suturing and only one case required chest tube placement. All patients evolved uneventfully. CONCLUSIONS: Repair of diaphragmatic injuries should always be attempted with intracorporeal suture since this is a feasible, reproducible and reliable technique.

Cirugía mínimamente invasiva en las reparaciones de las lesiones diafragmaticas / Minimal invasive surgery to repair diaphragmatic injuries

Objetivos: Describir la utilización de la cirugía mínimamente invasiva en la reparación de las lesiones diafragmáticas. Pacientes–Métodos: Entre Julio 1996 Noviembre 2003, 48 pacientes con trauma toracoabdominal no penetrante fueron sometidos en el servicio de cirugía general número 1, Hospital Miguel Pérez Carreño a video cirugía, (Laparoscopia 36-Toracoscopia 12). El diagnóstico se estableció por clínica, imagenología (RX-TAC-RMN) y se confirmó durante la laparoscopia o toracoscopia visualizándose el defecto y el paso del epiplón mayor y otras vísceras intrabdominales a la cavidad pleural. La restauración se efectuó mediante las suturas endoscópicas o mecánicas. Resultados: En el 75/100 el procedimiento fue por vía abdominal; y torácica el 25/100. El 83,33/100 de los lesionados pertenecían al sexo masculino, el 16,67/100 al femenino; edad promedio de 35 años rango 25 (23-48); Índice de trauma (APACHEII) de 11. 91,66/100 con lesiones diafragmáticas grado II y 8,34/100 grado III. El tiempo operatorio promedio de 58 minutos, rango 100 (20-120); la hospitalización desde el momento de la cirugía al egreso fue de 2.5 días, rango 4 (1-5 días); 4,16/100 de los pacientes intervenidos desarrollaron neumotórax a tensión y el 8,33/100 ateletasia. Conclusiones: La cirugía de las lesiones diafragmáticas mediante el video con las técnicas estandarizadas es una opción factible segura con mínima morbilidad-mortalidad.

Lesión traumática del diafragma / Traumatic lesion of the diafragm

Se presentan 31 casos de lesiones traumáticas del diafragma, 29 pertenecían al sexo masculino y 2 al femenino. Fueron penetrantes en 27 y cerradas en 4 casos. Todos los pacientes recibieron tratamiento quirúrgico en las primeras 24 horas. Las lesiones fueron unilaterales en todos los casos, 17 en el lado izquierdo y 14 en el derecho. En 29 traumatizados la lesión diafragmática fue un hallazgo intraoperatorio, solamente en 8 de ellos se sospechó el diagnóstico. El tipo de abordaje fue la laparotomía en 25 casos, seguida por la toracotomía, el abordaje combinado y la toraco-freno-laparotomía. En 29 casos se encontraron lesiones asociadas en otros órganos (hígado 15 casos, pulmón en 14, bazo en 6, grandes vasos y riñón en 5 cada uno, colon 4, estómago 3, páncreas 2). Se complicaron 6 pacientes (atelectasia homolateral 6, hemotórax 2 y empiema pleural 1). Fallecieron 4 pacientes, 2 en el intraoperatorio y 2 en el postoperatorio inmediato.

Paralysie phrenique apres chirurgie pediatrique: interet de la plicature diaphragmatique. A propos de deux cas

Phrenic nerve injury is a recognized and severe complication after cardiac surgery. Diaphragmatic paralysis leads to difficulty of weaning the child from the ventilator. Surgical plication is an easy and safe procedure that result in early clinical and physiological improvements

Drenagem anômala total das veias pulmonares: terapêutica cirúrgica dos tipos anatômicos infracardíaco e misto / Total anomalous pulmonary venous drainage: surgical therapy for the infradiaphragmatic and mixed anatomical types

OBJETIVO: Estudar a evolução hospitalar em portadores de drenagem anômala total de veias pulmonares (DATVP), nas formas infracardíaca e mista, submetidos a tratamento cirúrgico. MÉTODOS: De 65 pacientes operados com o diagnóstico isolado de DATVP, de dezembro/1993 a março/2002, foram selecionados, retrospectivamente, 7 (10,8 por cento) pacientes das formas mista e infradiafragmática, sendo 5 (71,4 por cento) do sexo masculino, idades variando de 5 dias a 19 (média de 7) meses, com diagnóstico clínico feito pelo ecocardiograma bidimensional. Quatro (57,1 por cento) pacientes apresentavam formas mistas, em um, obstrutiva intrínseca, com estenose discreta da veia inferior esquerda. Os restantes três (42,9 por cento) apresentavam a forma infradiafragmática obstrutiva, extrínseca ao nível do diafragma. Todas as operações foram realizadas através de esternotomia mediana, sob circulação extracorpórea hipotérmica com parada circulatória total em 2 casos. RESULTADOS: Obito hospitalar ocorreu em 1 paciente com DATVP infradiafragmática com conexão da veia vertical inferior com a veia porta. A causa mortis foi relacionada à falência de múltiplos órgãos e sistemas. O pós-operatório foi caracterizado pela presença de baixo débito cardíaco e hipertensão pulmonar em 4 (57,1 por cento) pacientes. CONCLUSAO: O resultado da correção cirúrgica desta anomalia está associado à morbidade e mortalidade aceitáveis, na dependência do encaminhamento e tratamento cirúrgico precoces, sem progressão do quadro de hipertensão vascular pulmonar.